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  <Article>
    <Journal>
      <PublisherName>jmedicalcasereports</PublisherName>
      <JournalTitle>Frontiers in Medical Case Reports</JournalTitle>
      <PISSN>I</PISSN>
      <EISSN>S</EISSN>
      <Volume-Issue>Volume 3; Issue 1</Volume-Issue>
      <PartNumber/>
      <IssueTopic>Multidisciplinary</IssueTopic>
      <IssueLanguage>English</IssueLanguage>
      <Season>(Jan-Feb, 2022)</Season>
      <SpecialIssue>N</SpecialIssue>
      <SupplementaryIssue>N</SupplementaryIssue>
      <IssueOA>Y</IssueOA>
      <PubDate>
        <Year>-0001</Year>
        <Month>11</Month>
        <Day>30</Day>
      </PubDate>
      <ArticleType>Medical Case Reports</ArticleType>
      <ArticleTitle>A Rare Case of Pulmonary Renal Syndrome Secondary to Microscopic Polyangiitis – A Case Report</ArticleTitle>
      <SubTitle/>
      <ArticleLanguage>English</ArticleLanguage>
      <ArticleOA>Y</ArticleOA>
      <FirstPage>1</FirstPage>
      <LastPage>5</LastPage>
      <AuthorList>
        <Author>
          <FirstName>Viraj</FirstName>
          <LastName>Shah</LastName>
          <AuthorLanguage>English</AuthorLanguage>
          <Affiliation/>
          <CorrespondingAuthor>N</CorrespondingAuthor>
          <ORCID/>
          <FirstName>Alexandra</FirstName>
          <LastName>Lacqua</LastName>
          <AuthorLanguage>English</AuthorLanguage>
          <Affiliation/>
          <CorrespondingAuthor>Y</CorrespondingAuthor>
          <ORCID/>
          <FirstName>Gregory</FirstName>
          <LastName>Demirjian</LastName>
          <AuthorLanguage>English</AuthorLanguage>
          <Affiliation/>
          <CorrespondingAuthor>Y</CorrespondingAuthor>
          <ORCID/>
          <FirstName>Akash</FirstName>
          <LastName>Patel</LastName>
          <AuthorLanguage>English</AuthorLanguage>
          <Affiliation/>
          <CorrespondingAuthor>Y</CorrespondingAuthor>
          <ORCID/>
          <FirstName>Dhruvil</FirstName>
          <LastName>Shah</LastName>
          <AuthorLanguage>English</AuthorLanguage>
          <Affiliation/>
          <CorrespondingAuthor>Y</CorrespondingAuthor>
          <ORCID/>
          <FirstName>Taaha</FirstName>
          <LastName>Mendha</LastName>
          <AuthorLanguage>English</AuthorLanguage>
          <Affiliation/>
          <CorrespondingAuthor>Y</CorrespondingAuthor>
          <ORCID/>
        </Author>
      </AuthorList>
      <DOI/>
      <Abstract>Diffuse Alveolar Hemorrhage (DAH) is one of the life-threatening pulmonary complications of AAV (ANCA-Associated Vasculitis). Pulmonary Renal Syndrome (PRS) is defined as concurrent autoimmune-induced DAH and Rapidly progressive glomerulonephritis (RPGN). Major organs involved in MPA (Microscopic Polyangiitis) are the kidneys and the lungs. The gold standard to confirm alveolar hemorrhage is bronchoalveolar lavage (BAL). We hereby describe a case in which our patient presented to the emergency room after being sent by his nephrologist for kidney biopsy in the setting of unexplained worsening renal functions. Patient ultimately developed PRS and was started on remission treatment with pulse dose steroids, plasmapheresis, and cyclophosphamide. Unfortunately, the patient deceased from multiorgan failure secondary to septic shock. PRS, once suspected, appropriate autoimmune workup should be undertaken, usually followed by renal biopsy.</Abstract>
      <AbstractLanguage>English</AbstractLanguage>
      <Keywords>AAV (ANCA-Associated Vasculitis),(PRS) Pulmonary Renal Syndrome</Keywords>
      <URLs>
        <Abstract>https://www.jmedicalcasereports.org/ubijournal-v1copy/journals/abstract.php?article_id=13583&amp;title=A Rare Case of Pulmonary Renal Syndrome Secondary to Microscopic Polyangiitis – A Case Report</Abstract>
      </URLs>
      <References>
        <ReferencesarticleTitle>References</ReferencesarticleTitle>
        <ReferencesfirstPage>16</ReferencesfirstPage>
        <ReferenceslastPage>19</ReferenceslastPage>
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      </References>
    </Journal>
  </Article>
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